Table 1.
Clinicopathological characteristics of patients.
| Factor | Overall Population (n = 115) n (%) | |
|---|---|---|
| Gender | female | 56 (48.7%) |
| male | 59 (51.3%) | |
| Age at first diagnosis | median (range) | 43.1 (18–82) |
| Age at start of systemic treatment | median (range) | 44 (18–84) |
| Location of primary tumor | Arm | 16 (13.9%) |
| Lower Distal | 16 (13.9%) | |
| Trunk | 21 (18.3%) | |
| Head and Neck | 7 (6.1%) | |
| Visceral | 6 (5.2%) | |
| Lower Proximal | 36 (31.3%) | |
| Retroperitoneal | 13 (11.3%) | |
| Grade | G1 | 5 (4.3%) |
| G2 | 30 (26.1%) | |
| G3/GX | 80 (69.6%) | |
| Primary tumor size | T1 (<5 cm) | 0 (0%) |
| T2 (5–10 cm) | 8 (7.0%) | |
| T3 (10–15 cm) | 52 (25.2%) | |
| T4 (>15 cm) | 19 (16.5%) | |
| unknown | 36 (31.3%) | |
| Histologic subtype | NOS | 109 (94.8%) |
| Epithelioid | 2 (1.7%) | |
| Malignant Triton tumor | 4 (3.5%) | |
| NF1—related MPNST | 23 (20.0%) | |
| Distant metastases at diagnosis | 10 (8.7%) | |
| Resection of the primary tumor | 97 (84.3%) | |
| Unresectable primary tumor without metastases | 11 (9.6%) | |
| Metastases location at the start of the systemic treatment | Lung | 72 (62.6%) |
| Liver | 6 (5.2%) | |
| Lymph nodes | 14 (12.2%) | |
| Bones | 7 (6.1%) | |
| Other | 10 (8.7%) | |
| Primary tumor/local recurrence | 58 (50.4%) | |
| Previous (perioperative chemotherapy) | 26 (22.6%) | |