Table 1.
Disease site | PDAI | ABSIS | PGA | ABQoL | ||||
---|---|---|---|---|---|---|---|---|
cutaneous score* | Mucosal score | Total activity score | cutaneous score | Mucosal score** | Total activity score | |||
All patients (IQR) | 2 (14) | 6 (10) | 13 (21.4) | 0.1 (3.1) | 12.5 (26.5) | 15.1 (26) | 3.33 (2.83) | 31 (15.5) |
Cutaneous (IQR)** | 13 (12.9) | 0 | 13 (12.9) | 3.17 (25.99) | 0 | 3.175 (25.99) | 3.16 (4.21) | 24.5 (22) |
Mucosal (IQR) | 0 | 7 (9.2) | 7 (9.2) | 0 | 17.5 (28.88) | 17.5 (28.88) | 2 (1.58) | 36 (5.5) |
Mucocutaneous (IQR) | 10 (23.8) | 6.3 (9) | 20 (24.5) | 2 .25 (6.76) | 15 (25.5) | 20.55 (22.86) | 4.16 (3) | 26 (14) |
*Sum of skin and scalp scores for PDAI score
**Sum of scores for oral involvement and severity was considered as mucosal score
Abbreviation: PDAI pemphigus disease area index, ABSIS Autoimmune Bullous Skin Disorder Intensity Score, ABQoL autoimmune bullous disease quality of life, PGA physician global assessment, IQR interquartile range