Table 1. Mutations in human plasmalemmal SLC1 transporters.
| Gene | Protein name | Missense coding variants | Transport phenotype | Traf ficking to target membrane | Disease phenotype | Mode of inheritance | OMIM# |
|---|---|---|---|---|---|---|---|
| SLC1A1 | EAAT3 | E48*, R445W, I395del | Loss-of-function | Reduced | Dicarboxylic aminoaciduria, autism | AR | 222730 |
| T164A | ? | ? | Obsessive compulsive disorder (OCD) and bipolar disorder | AD | |||
| R280C | ? | ? | Schizotypal personality disorder | SM | 615232 | ||
| SLC1A2 | EAAT2 | N206S | Loss-of-function | Reduced | Sporadic amyotrophic lateral sclerosis | AD | |
| L85P | Loss-of-function | Reduced | Epileptic encephalopathy | AD/CHet | 617105 | ||
| G82R, P289R, L474* | ? | ? | |||||
| A79G | ? | ? | Hereditary spastic paraplegia | AD | |||
| G6S, R31Q | ? | ? | Bipolar disorder and schizophrenia | AD | |||
| SLC1A3 | EAAT1 | P290R | Loss-of-function | Reduced | Episodic ataxia | AD | 612656 |
| C186S | Minimally reduced | Altered | |||||
| M128R, T318A, A329T1, V393I, R454Q, K520R | ? | ? | |||||
| T387P | Loss-of-function | Reduced | Hemiplegia migraines with aura | AD | |||
| A329T2 | ? | ? | Benign essential blepharospasm | AD | |||
| E219D | Gain-of-function | Increased | Tourette syndrome | AD | |||
| SLC1A4 | ASCT1 | E256K, R457W | Loss-of-function | Unaltered | Spastic tetraplegia, thin corpus callosum, and progressive | AR | 616657 |
| Y191*, L315Hfs*42, G381R,W453* | ? | ? | microcephaly; SPATCCM | ||||
AR: Autosomal recessive; AD: Autosomal dominant; CHet: Compound heterozygotes; SM: somatic mosaicism.