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. Author manuscript; available in PMC: 2023 Jun 7.
Published in final edited form as: Pract Neurol. 2022 Jul 11:practneurol-2021-003324. doi: 10.1136/practneurol-2021-003324

Box 1.

Clinical features in iSS (in order of most-to-least frequently reported)
Hearing loss
Imbalance
Gait/truncal ataxia
Pyramidal signs
Myelopathy-related symptoms (radiculopathy, pain, sensory disturbances)
Cognitive dysfunction
Bladder disturbance (incontinence, voiding difficulty, urgency, sensory abnormalities)
Bowel disturbances (constipation)
Symptoms of intracranial hypotension
Symptoms associated with arachnoiditis (lower back/sacral pain, sciatica pain)
Dysphagia
Hydrocephalus
Olfactory dysfunction
Ageusia
Myoclonus
Seizures
Visual disturbances
Cranial nerve palsies
Paraparesis/quadriparesis

Clinical features associated with infratentorial superficial siderosis (iSS) 1 4 6 10 27 28.