Table 2.
IPAF-related features.
| Clinical Domain | N = 39 (%) |
|---|---|
| Included in IPAF’s clinical criteria | |
| Mechanic’s hands | 5 (12.8%) |
| Digital ulcers | 1 (2.6%) |
| Arthritis or polyarticular morning stiffness ≥60min. | 32 (82.1%) |
| Palmar telangiectasias | 1 (2.6%) |
| Raynaud’s phenomenon | 10 (25.6%) |
| Digital oedema | 1 (2.6%) |
| Gottron’s sign | 4 (10.3%) |
| Not included in IPAF’s clinical criteria | |
| Sicca symptoms | 14 (35.9%) |
| Hair loss | 8 (20.5%) |
| Rash | 21 (53.8%) |
| Photosensitivity | 5 (12.8%) |
| Fever | 7 (18.4%) |
| Mouth ulcers | 1 (2.6%) |
| Serologic Domain | |
| ACPA | 2 (5.1%) |
| RF (≥ 2 x upper limit of normal) | 3 (7.7%) |
| ANA >1/320 | 23 (59%) |
| Anti-Ro/SSA | 8 (20.5%) |
| Anti-La/SSB | 2 (5.1%) |
| Anti-Sm | 0 |
| Anti-RNP | 1 (2.6%) |
| Anti-Jo1 | 3 (7.7%) |
| Other autoantibodies | 6 (15.4%) |
| Radiological pattern – Morphologic Domain | |
| NSIP | 24 (61.5%) |
| OP | 2 (5.1%) |
| NSIP-OP overlap | 2 (5.1%) |
| LIP | 1 (2.6%) |
| UIP | 7 (18%) |
| NSIP and UIP | 3 (7.7%) |