Age	Events
Past medical history: hypoplastic left heart syndrome, Norwood-OP (7days), Glenn-OP (3 months), extracardiac fenestrated Fontan-OP (3 years), closure of fenestration (3.5 years)
6 years	Diagnosis of protein-losing enteropathy (PLE) (total protein 3.6 mg/dL), IgG 86 mg/dL, leucopoenia (1.6 G/L), elevated random stool α-1 antitrypsin level
	Diagnosis of cytomegalovirus enterocolitis, treatment with ganciclovir improved hypoproteinaemia
7 years	Recurrence of PLE (hypoproteinaemia)
	Initial treatment with budesonide transiently increased protein levels but had to be removed due to side effects
8 years	Diagnosis of plastic bronchitis (PB) (dyspnoea, hypoxaemia, and coughing, removal of large branching casts during bronchoscopy)
8 years 1 month	Lymphatic imaging via the lymph nodes/patient was listed for heart transplantation
8 years 7 months	Thoracic duct decompression
	Protein levels increased from 34 mg/dL preoperatively up to 72 mg/dL during follow-up but oxygen saturation dropped after the operation from 92–96% to 76–80%
8 years 11 months	Banding of internal jugular vein
	After banding peripheral oxygen saturation (SpO2) was on average 85% in room air. Protein levels did not decrease
Follow-up 6 months after banding	No signs of PLE or PB. Fatigue improved. SpO2: 82%, total protein 70.4 mg/dL