Table 1.
Characteristics of adult-onset Still's disease (AOSD) patients, main areas of uptake represented at positron emission tomography (PET) scans, and type of therapy undertaken at time of scan.
Patient number | PET-computed tomography magnetic resonance (CT/MR) scans performed for each patient (total n = 23) | Pouchot's score | Main areas of organ uptake | Therapy | Supposed AOSD pattern |
---|---|---|---|---|---|
1 | 1 | 3 | LN, BM, spleen | Antibiotics | Polycyclic |
2 | 3 | LN, (spleen equal as liver) | Anakinra | ||
3 | 1 | No uptake | Anakinra | ||
2 | 1 | 2 | BM | na | Monocyclic |
3 | 1 | na | BAT | Corticosteroids | Monocyclic |
4 | 1 | 4 | BAT, LN | Anakinra | Polycyclic |
5 | 1 | 1 | Spleen, LN, BAT | Acetamynophen | Monocyclic |
6 | 1 | 3 | LN, BM | Acetamynophen | Polycyclic |
2 | 1 | No uptake | Corticosteroids | ||
7 | 1 | na | No uptake | na | Monocyclic |
8 | 1 | 4 | BM, spleen | Indomethacin | |
9 | 1 | 3 | BM | Corticosteroids/anakinra | Polycyclic |
10 | 1 | 5 | LN | Corticosteroids | Polycyclic/MAS |
2 | 6 | LN, BM, spleen | Anakinra/corticosteroids/ cyclosporin |
||
11 | 1 | na | No significant uptake | na | Monocyclic |
12 | 1 | 3 | BM | na | Monocyclic |
13 | 1 | 2 | BM | na | Polycyclic |
2 | na | LN | Anakinra | ||
14 | 1 | 3 | No significant uptake | Anakinra | Polycyclic |
15 | 1 | 6 | BM, LN, liver | Corticosteroids/cyclosporin | Polycyclic/MAS |
16 | 1 | na | Musculoskeletal diffuse uptake | Anakinra | Chronic articular |
17 | 1 | 5 | Spleen | na | Polycyclic |
18 | 1 | 3 | BM, liver | na | Monocyclic |
Legend: na, not available/no therapy; BAT, brown adipose tissue; BM, bone marrow; LN, lymph nodes.