Table 4.

Classification of EBV-associated T- and NK-cell lymphoproliferative diseases^19,20.

Disease
Aggressive NK-cell leukemia
Chronic active EBV infection (CAEBV) of T- and NK-cell type
Cutaneous CAEBV of T- and NK-cell type
Hydroa vacciniforme-like lymphoproliferative disease
Severe mosquito bite allergy
Systemic CAEBV of T- and NK-cell type
EBV-associated hemophagocytic lymphohistiocytosis
Extranodal NK/T-cell lymphoma, nasal type
Primary EBV+ nodal NK/T-cell lymphomaa
Systemic EBV+ T-cell lymphoma of childhood

^aA provisional entity.