Table 1.
Baseline Characteristics.
| Variables |
CTX group (n = 5) mean (STD) or frequency |
RTX group (n = 23) mean (STD) or frequency |
Group A (n = 10) mean (STD) or frequency |
p-value |
|---|---|---|---|---|
| Age (years) | 33 (7.80) | 44 (20.55) | 43 (13.4) | 0.44 |
| Gender (F/M) | 5/0 | 13/10 | 7/3 | 0.169 |
| Initial inhibitor level | 1.98 (2.50) | 2.97 (2.72) | 2.30 (2.51) | 0.73 |
| Initial ADAMTS13 antibody level | 37.5 (34.65) | 33.83 (29.08) | N/A | 0.89 |
| D-Dimer | 767.00 (202.34) | 2255.57 (1801.57) | 1590.75 (600.06) | 0.31 |
| Fibrinogen | 264.40 (67.42) | 302.95 (90.46) | 319.00 (117.66) | 0.63 |
| Nadir platelet count | 8.8 (2.28) | 12.5 (8.6) | 12.20 (7.36) | 0.64 |
| Absolute neutrophil count | 7.1 (4.72) | 8.8 (4.1) | 6.97 (2.14) | 0.55 |
| Absolute lymphocyte count | 1.61 (1.06) | 2.07 (1.05) | 1.91 (1.40) | 0.70 |
| Neutrophil-to-lymphocyte ratio | 9.59 (12.59) | 6.23 (5.85) | 5.61 (4.09) | 0.61 |
| Creatinine on admission | 1.02 (0.22) | 1.93 (1.98) | 3.03 (1.47) | 0.31 |
| Peak LDH on admission | 1,444.4 (790.47) | 1,222.91 (604.31) | 926.20 (374.53) | 0.41 |
| Platelet normalization (days) | 11.2 (7.73) | 11.32 (11.41) | 11.20 (16.13) | 0.99 |
| LDH normalization (days) | 11.6 (6.62) | 11.33 (10.6) | 6.00 (3.16) | 0.58 |
| Resolution time (days) | 14.6 (8.32) | 14.5 (12.07) | 12.80 (15.15) | 0.96 |
| Duration of hospitalization (days) | 23.6 (9.29) | 26.75 (15.98) | 11.2 (6.72) | 0.13 |
| Altered mental status (Yes/ No) | 2/3 | 8/13 | 2/2 | 0.91 |
| Autoimmune disease (Yes/No) | 3/2 | 3/20 | 2/8 | 0.07 |
| Malignancy (Yes/No) | 3/2 | 4/19 | 1/9 | 0.06 |