FIG 2.

DL-GNT with diffuse “cyst-like” foci of T2 prolongation involving the brain and spine. Coronal T2-weighted image of the brain (A) demonstrates numerous foci of T2 prolongation located predominantly along the leptomeningeal surfaces of the cerebellum. These did not enhance after contrast administration or suppress on FLAIR (not shown). Also seen is hydrocephalus with transependymal edema as evidenced by abnormal periventricular T2 prolongation. Sagittal T2-weighted image of the cervicothoracic spine (B) in a different patient shows numerous small cervicothoracic intramedullary cyst-like lesions expanding the spinal cord. These cyst-like lesions are very suggestive of DL-GNT.