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. 2020 Oct 29;10:566822. doi: 10.3389/fonc.2020.566822

Table 5.

Types of cancer associated with Li-Fraumeni Syndrome.

Cancer types in Li-Fraumeni Syndrome Prevalence (%)
Most frequent six “core” cancers Premenopausal Breast Cancer 27–31
Soft Tissue Sarcomas 17–27
Osteosarcoma 13.4–16
CNS Tumors 9–14
Adrenocortical Carcinoma 6–13
Leukemia 2–4
Other less frequent cancer types Myelodysplastic Syndrome
Lymphoma
Lung
Laryngeal
Thyroid
Gastrointestinal tract
Kidney
Testicular
Prostate
Ovarian
Skin
Neuroblastoma