Table 5.
Types of cancer associated with Li-Fraumeni Syndrome.
Cancer types in Li-Fraumeni Syndrome | Prevalence (%) | ||
---|---|---|---|
Most frequent six “core” cancers | Premenopausal Breast Cancer | 27–31 | |
Soft Tissue Sarcomas | 17–27 | ||
Osteosarcoma | 13.4–16 | ||
CNS Tumors | 9–14 | ||
Adrenocortical Carcinoma | 6–13 | ||
Leukemia | 2–4 | ||
Other less frequent cancer types | Myelodysplastic Syndrome Lymphoma Lung Laryngeal |
Thyroid Gastrointestinal tract Kidney Testicular |
Prostate Ovarian Skin Neuroblastoma |