Table 5.
Types of cancer associated with Li-Fraumeni Syndrome.
| Cancer types in Li-Fraumeni Syndrome | Prevalence (%) | ||
|---|---|---|---|
| Most frequent six “core” cancers | Premenopausal Breast Cancer | 27–31 | |
| Soft Tissue Sarcomas | 17–27 | ||
| Osteosarcoma | 13.4–16 | ||
| CNS Tumors | 9–14 | ||
| Adrenocortical Carcinoma | 6–13 | ||
| Leukemia | 2–4 | ||
| Other less frequent cancer types | Myelodysplastic Syndrome Lymphoma Lung Laryngeal |
Thyroid Gastrointestinal tract Kidney Testicular |
Prostate Ovarian Skin Neuroblastoma |