| ER | Endoplasmic Reticulum |
| JNCL | Juvenile Neuronal Ceroid Lipofuscinosis |
| NCLs | Neuronal Ceroid Lipofuscinoses |
| mPTP | Mitochondrial Permeability Transition Pore |
| ROS | Reactive Oxygen Species |
| ER | Endoplasmic Reticulum |
| JNCL | Juvenile Neuronal Ceroid Lipofuscinosis |
| NCLs | Neuronal Ceroid Lipofuscinoses |
| mPTP | Mitochondrial Permeability Transition Pore |
| ROS | Reactive Oxygen Species |