Table 5.

Relevant causes of vomiting in metabolic disorders.

ASSOCIATED OR NOT WITH ENCEPHALOPATHY
Organic acidurias
Urea cycle disorders
Fatty acid oxidation disorders
MCT1 defect
MELAS
Glutaric aciduria type I
ASSOCIATED WITH ACIDOSIS/KETOACIDOSIS
Organic acidurias
Mitochondrial diseases
ASSOCIATED WITH KETOSIS ONLY
Ketolysis defects
ASSOCIATED WITH SEVERE ABDOMINAL PAIN
Phorphyrias (acute intermittent porphyria, coproporphyria)
ASSOCIATED WITH HEPATOPATHY
Organic acidurias
Urea cycle disorders
Galactosemia
Hereditary fructose intolerance
Tyrosinemia type I
Fatty acid oxidation disorders