(A) Summary of phenotypes observed in mouse embryos with the indicated genotypes (e13.5–14.5). Dex, dextrocardia; Lev, levocardia; LPI, left pulmonary isomerism; PDD, preaxial digit duplication; RPI, right pulmonary isomerism; SIT, situs inversus; SS, situs solitus. A detailed list of phenotypes observed in each embryo can be found in Tables S2, S3, and S4.
(B) Representative light microscopy and ECM images of the developing lungs and limbs of single (control) and double heterozygous embryos. The normal right lung has 4 lobes (1R, 2R, 3R and 4R) and the left lung has one lobe (1L). Asterisks (*) mark the duplicated preaxial digits.
(C) Representative necropsy images showing the position of the heart, symmetry of the liver, and location of the stomach in single (control) and double heterozygous embryos. Arrow (top row) denotes the direction of the cardiac apex. See also Tables S2, S3, and S4.