Table 1.

Clinical information on the patient in the current study diagnosed with immunoglobulin G4-related optic perineuritis and on patients with this disease in two previous studies on cases

Case	Age at presentation (years)	Sex	Cranial nerve involvement	Visual acuity at presentation	Serum IgG4 level (normal < 135) mg/dL	Treatment	Visual acuity at final follow-up visit	Orbital involvement	Extra orbital involvement	Malignancy
Lee et al. (2015) [7]	54	Male	Possible enhancement along right optic nerve sheath	No light perception in both eyes	148	Oral corticosteroids followed by methotrexate	Bare light perception in both eyes	No	Hypertrophic pachymeningitis, chronic subdural hematoma, recurrent sinusitis	No
Lemaitre et al. (2018) [8]	78	Caucasian male	Bilateral optic perineuritis	20/20 in the right eye, 20/40 in the left eye	71 (within normal limits)	Oral corticosteroids followed by rituximab	20/50 in the right eye, counting fingers in the left eye	Right orbital fat, lateral and medial rectus muscles involvement	Pansinusitis	Subsequently died due to colon cancer with liver metastasis
This case report (2020)	38	Asian male	Bilateral optic perineuritis, bilateral maxillary nerves with perineural spreading to the infraorbital nerves	20/30 in the right eye, 20/40 in the left eye	2650	Oral corticosteroids followed by azathioprine	20/20 in the right eye, 20/25 in the left eye	Enlargement of bilateral inferior rectus, right medial rectus, bilateral superior rectus, and bilateral lateral rectus muscles	Pansinusitis	No

IgG4 Immunoglobulin G4