Table 1.
Control | IBM | FSHD | OPMD | P | |
N | 12 | 8 | 13 | 14 | |
Age (years) | 53.8±1.7 | 58.5±1.8 | 53.2±1.4 | 51.8±1.9 | 0.101 |
Sex | 6M/6F | 7M/1F | 6M/7F | 6M/8F | 0.196 |
BMI (cm/m2) | 27.3±1.5 | 26.6±0.6 | 25.3±1.1 | 25.7±1.1 | 0.693 |
Disease duration (years) | N/A | 6.4±2.5 | 28.5 ± 3.5 *** | 10.2±2.5 | <0.001 |
MRC score | |||||
Quadriceps | 5.0±0.0 | 4.0 ± 0.9 ** | 5.0±0.8 | 5.0±0.0 | 0.003 |
Tibialis anterior | 5.0±0.0 | 4.5 ± 0.8 ** | 4.5±3.0 | 5.0±0.0 | 0.005 |
CK (U/L) | 136.3±24.6 | 772.3 ± 261.1 ** | 263.0±31.3 | 292.8±76.5 | 0.002 |
Data are reported as mean±SEM for continuous data, and median±IQR for ordinal data. Abbreviations: CK: creatine kinase. IBM: inclusion body myositis. FSHD: facioscapulohumeral muscular dystrophy. OPMD: oculopharyngeal muscular dystrophy. *p < 0.05, **p < 0.01, ***p < 0.001.