表 1.
17例RPF患者临床特点
Clinical features at presentation in 17 patients with RPF
| Clinical Features | n (%) |
| CRP, C-reactive protein; ESR, erythrocyte sedimentation rate; Ig, immunoglobin; HPF, high power field. | |
| Gender | |
| Male | 12 (70.6) |
| Female | 5 (29.4) |
| Symptoms | |
| Back pain | 9 (52.9) |
| Abdominal pain | 6 (35.3) |
| Oliguria | 2 (11.8) |
| Lower limb edema | 3 (17.6) |
| Diarrhea | 1 (5.9) |
| Constipation | 1 (5.9) |
| Laboratory studies | |
| Increased CRP | 13 (76.5) |
| Increased ESR | 13 (76.5) |
| Increased IgG4 | 5 (29.4) |
| Increased IgG (n=13) | 4 (30.8) |
| Increased IgM (n=13) | 0 |
| Increased IgE (n=13) | 4 (30.8) |
| Increased IgA (n=13) | 1 (7.7) |
| Decreased C3 (n=13) | 1 (7.7) |
| Decreased C4 (n=13) | 1 (7.7) |
| Hydronephrosis | |
| Left hydronephrosis | 8 (47.1) |
| Right hydronephrosis | 1 (5.9) |
| Bilateral hydronephrosis | 8 (47.1) |
| Radiographic class | |
| Ⅰ+Ⅱ+Ⅲ | 14 (82.4) |
| Ⅰ+Ⅱ+Ⅲ+Ⅳ | 3 (17.6) |
| Pathological features (n=12) | |
| < 10 IgG4+ plasma cells/HPF | 6 (50.0) |
| 10-30 IgG4 + plasma cells/HPF | 2 (16.7) |
| > 30 IgG4 + plasma cells/HPF | 4 (33.3) |
| IgG4+/IgG+ plasma cell ratio > 40% | 4 (33.3) |
| Storiform-type fibrosis | 3 (25.0) |
| Obliterative phlebitis | 4 (33.3) |