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. Author manuscript; available in PMC: 2021 Sep 3.
Published in final edited form as: Mol Genet Metab. 2020 Sep 3;131(1-2):267–276. doi: 10.1016/j.ymgme.2020.08.006

Figure 1. Kidney and liver survival rates based on age at organ transplantation.

Figure 1.

Figure 1.

A) Percent kidney survival of the entire cohort of 73 patients. B) Kidney survival rates in males and females. C) Kidney survival rates in patients with “truncating” and “non-truncating” PKHD1 variants D) Kidney survival rates in patients who became symptomatic perinatally in comparison to those who presented after 1 month of age. E) Kidney survival rates in patients with “corticomedullary” disease compared to those with “medullary” disease. F) Liver survival of the entire cohort of 73 patients. G) Liver survival rates in males and females. H) Liver survival rates in patients with missense (“non-truncating”) and “truncating” PKHD1 variants.