Table 3.

Characteristics of liver disease in 73 ARPKD patients evaluated at the NIH Clinical Center^€.

	Number (%)
Portal Hypertension	51 of 72* (71)
Males with portal hypertension	25 of 51
Females with portal hypertension	26 of 51
Esophagogastroduodenoscopy performed	45 of 72 (63)
Esophageal Varices	31 of 45 (69)
Variceal Banding	17 of 31 (55)
Variceal Bleeding	6 of 31 (19)
First visit Liver Echogenicity Normal/Mildly Increased	21 of 72 (29)
First Visit Liver Echogenicity Moderately/Severely Increased	51 of 72 (71)
Liver echogenicity progressed during the study	14 of 72 (19)
First visit Intrahepatic Cysts	29 of 72 (40)
First Visit Dilated Common Bile Duct	38 of 71 (54)
Biliary cystic disease progressed during the study	20 of 57 (35)
Cholangitis**	10 of 73 (14)

^€This table presents data on all patients evaluated under this study (13 with single and 60 with multiple visits).

^*One patient with hereditary spherocytosis was excluded.

^**Four out of 10 patients had recurrent cholangitis.