Table 2.
The clinical course of cystic fibrosis in the followed patients (n=116)
| Disorders during the monitoring | No. of patients | % |
| Respiratory disorders: | ||
| • Bronchiectatsis | 67 | 57.8 |
| • Pseudomonas Aeruginosa chronic colonization | 55 | 47.4 |
| • Chest wall depression or protrusion | 38 | 32.8 |
| • Clubbing | 37 | 31.9 |
| • Chronic respiratory failure | 31 | 26.7 |
| • Pulmonary arterial hypertension | 10 | 8.6 |
| • Hemoptysis | 9 | 7.8 |
| • Pneumothorax | 4 | 3.4 |
| • Allergic bronchopulmonary aspergillosis | 3 | 2.6 |
| Extra-respiratory disorders: | ||
| • Hypotrophy (weight < -2SD) | 65 | 56 |
| • Hepatomegaly / Cholestasis | 15 | 12.9 |
| • Cirrhosis | 4 | 3.4 |
| • Pansinusitis / Nasal polyposis | 4 | 3.4 |
| • Diabetes | 4 | 3.4 |
| • Osteoporosis | 2 | 1.7 |