Hb genotype |
|
HbSS |
346 (93.0) |
HbSC |
26 (7.0) |
Age at diagnosis (year(s)) |
|
≤1 |
264 (71.0) |
2 |
61 (16.4) |
3 |
25 (6.7) |
≥4 |
22 (5.9) |
Range (0.5‐11.0 years) |
|
Clinic attendance |
|
Regular |
334 (89.8) |
Missed some appointments |
38 (10.2) |
Adherence to prophylactic medications |
|
Yes |
370 (99.5) |
No |
2 (0.5) |
Vaso‐occlusive crises requiring medication or visit to health facility |
|
Ever occurrence of vaso‐occlusive crisis (VOC) |
|
Yes |
272 (73.1) |
No |
100 (26.9) |
VOC episodes within preceding 12 months |
|
0 |
9 (3.3) |
1 |
36 (13.2) |
2 |
37 (13.6) |
≥3 |
190 (69.9) |
Ever hospitalized for VOC |
|
Yes |
153 (41.1) |
No |
219 (58.9) |
Frequency of hospitalization for VOC in the past |
|
0 |
219 (58.9) |
1 |
64 (17.2) |
2 |
10 (2.7) |
≥3 |
79 (21.2) |
Hospitalized for VOC in preceding 12 months |
|
Yes |
153 (41.1) |
No |
219 (58.9) |
Anemic crises |
|
Ever occurrence of anemic crisis requiring blood transfusion |
|
Yes |
170 (45.7) |
No |
202 (54.3) |
Episodes of anemic crisis requiring blood transfusion in the past |
|
0 |
202 (54.3) |
1 |
94 (25.3) |
2 |
32 (8.6) |
≥3 |
44 (11.8) |
Anemic crisis requiring blood transfusion in the preceding 12 months |
|
0 |
246 (66.1) |
1 |
90 (24.2) |
≥2 |
36 (9.7) |
Experienced both VOC and anemic crisis in the past |
|
Yes |
147 (39.5) |
No |
225 (60.5) |
Experienced both VOC and anemic crisis in the preceding 12 months |
|
Yes |
108 (29.0) |
No |
264 (71.0) |