Figure 2. Suggested algorithm for genetic testing of KDUE.
Patients in which a genetic disease is suspected can be tested as outlined. Secondary analyses may clarify negative results or VUS. Cases without positive results should be periodically reviewed and reanalyzed.
* CNV analysis is possible with exome data and is offered by some commercial testing laboratories, although CMA generally has higher sensitivity.</p/> ** ES may miss some SNVs, exons or entire genes due to variability in capture and coverage. ES may also miss CNVs, moderate sized deletions/duplications, retrotransposition, and deep intronic splice variants.
