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. 2021 Jan 2;22(1):411. doi: 10.3390/ijms22010411

Table 1.

WHO classification of mastocytosis *.

Cutaneous mastocytosis (CM)
   maculopapular cutaneous mastocytosis (MPCM) = urticaria pigmentosa (UP)
   diffuse cutaneous mastocytosis (DCM)
   Mastocytoma of skin (cutaneous mastocytoma)
Systemic mastocytosis (SM)
   Indolent systemic mastocytosis (ISM)
   Smoldering systemic mastocytosis (SSM)
   Systemic mastocytosis with associated hematologic neoplasm (SM-AHN)
   Aggressive Systemic mastocytosis (ASM)
Mast cell leukemia (MCL)
Mast cell sarcoma (MCS)

* The WHO classification of mastocytosis was updated in 2016 [9,10,11].