| ATF6 | Activating transcription factor 6 |
| BiP/Grp78 | Binding immunoglobulin protein |
| CBL | Cerebellum |
| CNS | Central Nervous System |
| DAB | Diaminobenzidine |
| ER | Endoplasmic Reticulum |
| ERAD | Endoplasmic Reticulum Associated Degradation |
| FC | Frontal Cortex |
| GFAP | Glial fibrillary acidic protein |
| Hc | Hippocampus |
| Ht | Hypothalamus |
| IRE1 | Inositol-requiring enzyme 1 |
| Mes | Mesencephalon |
| Mo | Medulla oblongata |
| PERK | PKR-like endoplasmic reticulum kinase |
| PDI | Protein disulfide isomerase |
| PrPSc | Pathological prion protein |
| PrPC | Cellular prion protein |
| Sa | Septal Area |
| PSP | Progressive Supranuclear Palsy |
| sCJD | Sporadic Creutzfeldt-Jakob Disease |
| T | Thalamus |
| TC | Cortex at the level of the thalamus |
| Tg | Transgenic |
| TSE | Transmissible Spongiform Encephalopathies |
| Ub | Ubiquitin |
| UPR | Unfolded Protein Response |
| UPS | Ubiquitin-Proteasome System |
| vCJD | Variant Creutzfeldt-Jakob Disease |