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. 2020 Aug 26;159(1):311–327. doi: 10.1016/j.chest.2020.07.088

Figure 1.

Figure 1

WHO Group 1 classification by clinical criteria on enrollment in the National Biological Sample and Data Repository for PAH and change in classification when United States Pulmonary Hypertension Scientific Registry genomic mutational data are included. Individuals previously classified as FPAH without identified mutations are included in the new HPAH classification. Original APAH subgroups are delineated in the lower chart. APAH = associated pulmonary arterial hypertension; CHD = congenital heart disease; CTD = connective tissue disease; FPAH = familial pulmonary arterial hypertension; HPAH = heritable pulmonary arterial hypertension; IPAH = idiopathic pulmonary arterial hypertension; PAH = pulmonary arterial hypertension; PCH = pulmonary capillary hemangiomatosis; PoPH = portopulmonary hypertension; PVOD = pulmonary venoocclusive disease; WHO = World Health Organization.