Table 1.

Organ involvement in IgG4-RD (from Della-Torre et al., modified [2].

Head and neck
Orbits and periorbital tissue	IgG4-related orbital disease
Salivary and lacrimal glands	IgG4-related sialadenitis
Thyroid	IgG4-related thyroiditis
Ear, nose, throat	IgG4-related sinusitis
Thorax
Lungs	IgG4-related lung disease
Pleura	IgG4-related pleural disease
Mediastinum	IgG4-related mediastinitis
Breast	IgG4-related mastitis
Abdomen and pelvis
Retroperitoneum	IgG4-related retroperitoneal fibrosis
Pancreas	IgG4-related pancreatitis
Biliary tree	IgG4-related sclerosing cholangitis
Liver	IgG4-related autoimmune hepatitis
Kidney	IgG4-related tubule-interstitial nephritis/glomerulonephritis
Gastrointestinal tract	IgG4-related gastrointestinal disease
Mesentery	IgG4-related sclerosing mesenteritis
Prostate	IgG4-related prostatitis
Testis	IgG4-related epididymitis-orchitis
Nervous system
Pituitary gland	IgG4-related hypophysitis
Peripheral nerves	IgG4-related neuropathy
Meninges	IgG4-related pachymeningitis
Cardiovascular system
Heart and pericardium	IgG4-related cardiac disease
Aorta	IgG4-related periaortitis
Lymph nodes	IgG4-related lymph adenopathy
Skin	IgG4-related skin disease
Bone	IgG4-related disease of the bone