Table 3.
IgG4-RD cohorts published in the literature.
| Author | Year | Country | N. pts | M:F ratio | Age at onset | Organ involvement | Serum IgG4 >135 mg/dl | |
|---|---|---|---|---|---|---|---|---|
| Ebbo49 | 2012 | France | 25 | 2.6:1 | 58 | Lymph nodes, pancreas | 100% | French registry |
| Fernandez-Codina50 | 2015 | Spain | 55 | 3:1 | 56 | Retroperitoneum, orbital pseudotumor | – | Spanish registry |
| Lin51 | 2015 | China | 118 | 2.3:1 | 53.1 | Pancreas, lymph nodes, salivary glans | 97.5% | Prospective, multicentre |
| Wallace52 | 2015 | USA | 125 | 1.6:1 | 50.3 | Pancreas, lymph nodes, submandibular glands | 51.4% | Retrospective, single centre |
| Quero53 | 2019 | Spain | 15 | 4:1 | 60.7 | Pancreas, lymph nodes, Kidney, salivary glands, lungs, vascular system | – | Retrospective, single centre |
| Campochiaro54 | 2016 | Italy | 41 | 1.9:1 | 62 | Pancreas, retroperitoneum | 73% | Retrospective, single centre |
| Li55 | 2017 | Hong Kong | 104 | 3:1 | 62 | Hepatobiliary system, lungs, retroperitoneum, CNS, eye, skin | 95% | Retrospective, single centre |
| Fong56 | 2018 | Singapore | 42 (35 definite) | 2.9:1 | 66.3 | Pancreas, lymph nodes, bile ducts | 77.5% | Retrospective, single centre |
| Inoue57 | 2015 | Japan | 235 | 4:1 | 67 | Pancreas, salivary glands, kidney | 88% | Retrospective multicentre |
| Wang58 | 2019 | China | 403 | 1.69:1 | 55 | Salivary glands, pancreas, Lung, retroperitoneum, kidney, lymph nodes, liver, gastrointestinal tract, skin, prostate, sinus, orbits, thyroid | – | Prospective |
| Jamada59 | 2017 | Japan | 334 | 1.5:1 | 63.8 | Salivary and lacrimal glands, lymph nodes, retroperitoneum/periaorta, lung, prostate, biliary tree, skin, thyroid | 95% | Retrospective multicentre |