Table 5.
Type IgG4-SCa | Isolated IgG4-SC | PSC [93] | Recurrent pyogenic cholangitis |
---|---|---|---|
Type1: involvement of lower part of bile duct only Type 2a: involvement of distal bile duct and intrahepatic bile duct with proximal dilation Type 2b: involvement of distal bile duct and diffuse intrahepatic bile duct without proximal dilation Type 3: involvement of distal bile duct and ducts at hepatic hilum Type 4: involvement of ducts at hepatic hilum only |
Absence of intra-hepatic bile ducts, bile duct lesions. Cholangiographic findings based on Nakazawa classificationa | Ductal irregularities of the intra- and extra hepatic biliary tree. Stenosis and saccular dilations (beaded appearance). Pruned-tree appearance at chronic stage |
Dilated intrahepatic bile ducts, bile duct strictures, calculi within dilated bile ducts and morphologic changes like atrophy |
Nakazawa classification [92].