Table 3.
Characteristics of Patients with Multivessel Pulmonary Vein Stenosis.
| Characteristics | PVS (n = 17) | No PVS (n = 51) | p-Value |
|---|---|---|---|
| Gestational age at birth | 35 (34, 38) | 38 (37, 38) | <0.01 |
| Sex (female) | 10 (59%) | 24 (47%) | 0.41 |
| Anatomy | |||
| CAVC | 12 (71%) | 36 (70%) | N/A |
| Secundum ASD | 3 (18%) | 10 (20%) | N/A |
| Membranous VSD | 2 (12%) | 5 (10%) | N/A |
| Surgical history | |||
| Primary repair | 15 (88%) | 51 (100%) | 0.01 |
| Palliation with PA band | 2 (12%) | 0 | 0.01 |
| Age at primary repair | 5 (3.5, 8.5) | 3 (2, 7) | 0.07 |
| Death | 4 (24%) | 0 | <0.01 |
| Pulmonary vein disease | |||
| Age at diagnosis (months) | 5.4 (3.9, 8.6) | N/A | N/A |
| Number of surgeries | 1 (0, 2) | N/A | N/A |
| Number of catheterizations | 1 (0, 15) | N/A | N/A |
| Pulmonary hypertension | |||
| Clinical diagnosis | 13 (76%) | 1 (2%) | <0.01 |
| Mean PA pressure > 25 mmHg | 8 (74%) | 0 | <0.01 |
| Sildenafil or oxygen | 13 (76%) | 0 | <0.01 |
All data is presented at numbers (percentages) or median (interquartile range), except for the number of surgery and catheter interventions, which includes the total range in parenthesis.