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. 2021 Jan 18;22(2):904. doi: 10.3390/ijms22020904
ALS Amyotrophic lateral sclerosis
arcRNA Architectural RNA
Arg Arginine
ATP Adenosine triphosphate
Aub Aubergine
BMAA β-N-methylamino l-alanine
C9ORF72 Chromosome 9 open reading frame 72
Ca Calcium
Cas9 CRISPR-associated protein 9
Caz Cabeza
CCAP Crustacean cardioactive peptide
Chip Chromatin immunoprecipitation
CNS Central nervous system
CRISPR Clustered regularly interspaced short palindromic repeats
Cu Copper
DART5 Drosophila arginine methyltransferase protein 5
dDSIF Drosophila DRB sensitivity-inducing factor
dEAAT1 Drosophila excitatory amino acid transporter 1
dFMR1 Drosophila Fragile X mental retardation 1
dFMRP Drosophila Fragile X mental retardation protein
Dlg Discs-large
DNA Deoxyribonucleic acid
dPAF1 Drosophila polymerase-associated factor 1
DPR Dipeptide proteins
eIF1A Eukaryotic translation initiation factor 1A
eIF2α Eukaryotic initiation factor 2α
EJP Excitatory junction potential
Elav Embryonic lethal abnormal visual protein
ER Endoplasmic reticulum
EWS Ewing sarcoma
fALS Familial amyotrophic lateral sclerosis
FET FUS EWS TAF15 family of proteins
FUS Fused in sarcoma
FTD Frontotemporal dementia
Gad1 Glutamic acid decarboxylase 1
GDP Guanosine diphosphate
GFP Green fluorescent protein
GluRIIA Glutamate receptor IIA
Gly Glycine
GMR Glass multiple reporter
GOF Gain of function
GRD Glycine-rich domain
GS GeneSwitch
GTP Guanosine triphosphate
HDAC6 Histone deacetylase 6
HEK/HEK293 Human embryonic kidney 293
HeLa Henrietta Lacks
Hpo Hippo
hnRNP Heterogenous nuclear ribonucleoprotein
HSP60 Heat-shock protein 60
HSP70 Heat-shock protein 70
HRE Hexanucleotide repeat expansion
IP3 Inositol 1,4,5-trisphosphate
iPSC Induced pluripotent stem cell
ITPR1 Inositol-1,4,5-trisphosphate receptor type 1
JNK c-Jun N-terminal kinase
Kapβ2 Karyopherin-β2
kDa Kilodalton
mTORC1 Mammalian target of rapamycin complex 1
LA α-Lipoic acid
LAMP-1 Lysosomal-associated membrane protein 1
LCD Low-complexity domain
lncRNA Long non-coding RNA
LOF Loss of function
MARCM Mosaic analysis with a repressible cell marker
miRNA MicroRNAs
mRNA Messenger RNA
NB Nuclear body
NES Nuclear export signal
NIR Nuclear import receptor
NMJ Neuromuscular junction
NLS Nuclear localization signal
Nup Nucleoporin
Orz γ-Oryzanol
PABPN1 Poly(A)-binding protein nuclear 1
PARG Poly(ADP-ribose) glycohydrolase
PARP1 Poly(ADP-ribose)ylation polymerase 1
PEK Poly(ADP-ribose)ylation glycohydrolase
PINK1 PTEN-induced kinase 1
piRNA Piwi-interacting RNA
PrLD Prion-like domain
poly-GA Poly-glycine/alanine
poly-GP Poly-glycine/proline
poly-GR Poly-glycine/arginine
poly-PA Poly-proline/alanine
poly-PR Poly-proline/arginine
PTM Post-translational modification
PTP1B Tyrosine phosphatase 1B
qPCR Quantitative polymerase chain reaction
QGSY Glutamine, glycine, serine, and tyrosine residues
RAN Repeat-associated non-AUG
RanGAP Ras-related nuclear GTPase-activating protein
RAVER1 Ribonucleoprotein, PTB-binding 1
RBP RNA-binding protein
Rbp1 RNA-binding protein 1
RGG Arginine glycine rich domain
ROS Reactive oxygen species
RRM RNA recognition motif
RNA Ribonucleic acid
RNAi RNA interference
RTE Retrotransposable element
RT-PCR Reverse transcriptase polymerase chain reaction
sALS Sporadic amyotrophic lateral sclerosis
SF2 Splicing factor 2
Sf3b-1 Splicing factor 3b subunit 1
SG Stress granule
siRNA Small interfering RNA
SOD Superoxide dismutase
SOP Sensory organ precursor
TAF15 TATA box-binding protein-associated factor 68 kDa
TARDBP TAR DNA-binding protein
TARGET Temporal and regional gene expression targeting
TBPH TAR DNA-binding protein-43 homolog
TCERG1 Transcription elongation regulator 1
TDP-43 TAR DNA-binding protein 43
TDPBR TDP-43 binding region
Ter94 Transitional endoplasmic reticulum 94
TLS Translocated in liposarcoma
TMPyP4 5,10,15,20-Tetrakis-(N-methyl-4-pyridyl)porphine
UAS Upstream activating sequence
UBPY Ubiquitin isopeptidase Y
UPR Unfolded protein response
UTR Untranslated transcribed region
VCP Valosin-containing protein
Wnd Wallenda
WT Wildtype
XPO1 Exportin 1
Zfp106 Zing finger protein 106
Zn Zinc
ZnF Zinc finger domain