| ALS | Amyotrophic lateral sclerosis |
| arcRNA | Architectural RNA |
| Arg | Arginine |
| ATP | Adenosine triphosphate |
| Aub | Aubergine |
| BMAA | β-N-methylamino l-alanine |
| C9ORF72 | Chromosome 9 open reading frame 72 |
| Ca | Calcium |
| Cas9 | CRISPR-associated protein 9 |
| Caz | Cabeza |
| CCAP | Crustacean cardioactive peptide |
| Chip | Chromatin immunoprecipitation |
| CNS | Central nervous system |
| CRISPR | Clustered regularly interspaced short palindromic repeats |
| Cu | Copper |
| DART5 | Drosophila arginine methyltransferase protein 5 |
| dDSIF | Drosophila DRB sensitivity-inducing factor |
| dEAAT1 | Drosophila excitatory amino acid transporter 1 |
| dFMR1 | Drosophila Fragile X mental retardation 1 |
| dFMRP | Drosophila Fragile X mental retardation protein |
| Dlg | Discs-large |
| DNA | Deoxyribonucleic acid |
| dPAF1 | Drosophila polymerase-associated factor 1 |
| DPR | Dipeptide proteins |
| eIF1A | Eukaryotic translation initiation factor 1A |
| eIF2α | Eukaryotic initiation factor 2α |
| EJP | Excitatory junction potential |
| Elav | Embryonic lethal abnormal visual protein |
| ER | Endoplasmic reticulum |
| EWS | Ewing sarcoma |
| fALS | Familial amyotrophic lateral sclerosis |
| FET | FUS EWS TAF15 family of proteins |
| FUS | Fused in sarcoma |
| FTD | Frontotemporal dementia |
| Gad1 | Glutamic acid decarboxylase 1 |
| GDP | Guanosine diphosphate |
| GFP | Green fluorescent protein |
| GluRIIA | Glutamate receptor IIA |
| Gly | Glycine |
| GMR | Glass multiple reporter |
| GOF | Gain of function |
| GRD | Glycine-rich domain |
| GS | GeneSwitch |
| GTP | Guanosine triphosphate |
| HDAC6 | Histone deacetylase 6 |
| HEK/HEK293 | Human embryonic kidney 293 |
| HeLa | Henrietta Lacks |
| Hpo | Hippo |
| hnRNP | Heterogenous nuclear ribonucleoprotein |
| HSP60 | Heat-shock protein 60 |
| HSP70 | Heat-shock protein 70 |
| HRE | Hexanucleotide repeat expansion |
| IP3 | Inositol 1,4,5-trisphosphate |
| iPSC | Induced pluripotent stem cell |
| ITPR1 | Inositol-1,4,5-trisphosphate receptor type 1 |
| JNK | c-Jun N-terminal kinase |
| Kapβ2 | Karyopherin-β2 |
| kDa | Kilodalton |
| mTORC1 | Mammalian target of rapamycin complex 1 |
| LA | α-Lipoic acid |
| LAMP-1 | Lysosomal-associated membrane protein 1 |
| LCD | Low-complexity domain |
| lncRNA | Long non-coding RNA |
| LOF | Loss of function |
| MARCM | Mosaic analysis with a repressible cell marker |
| miRNA | MicroRNAs |
| mRNA | Messenger RNA |
| NB | Nuclear body |
| NES | Nuclear export signal |
| NIR | Nuclear import receptor |
| NMJ | Neuromuscular junction |
| NLS | Nuclear localization signal |
| Nup | Nucleoporin |
| Orz | γ-Oryzanol |
| PABPN1 | Poly(A)-binding protein nuclear 1 |
| PARG | Poly(ADP-ribose) glycohydrolase |
| PARP1 | Poly(ADP-ribose)ylation polymerase 1 |
| PEK | Poly(ADP-ribose)ylation glycohydrolase |
| PINK1 | PTEN-induced kinase 1 |
| piRNA | Piwi-interacting RNA |
| PrLD | Prion-like domain |
| poly-GA | Poly-glycine/alanine |
| poly-GP | Poly-glycine/proline |
| poly-GR | Poly-glycine/arginine |
| poly-PA | Poly-proline/alanine |
| poly-PR | Poly-proline/arginine |
| PTM | Post-translational modification |
| PTP1B | Tyrosine phosphatase 1B |
| qPCR | Quantitative polymerase chain reaction |
| QGSY | Glutamine, glycine, serine, and tyrosine residues |
| RAN | Repeat-associated non-AUG |
| RanGAP | Ras-related nuclear GTPase-activating protein |
| RAVER1 | Ribonucleoprotein, PTB-binding 1 |
| RBP | RNA-binding protein |
| Rbp1 | RNA-binding protein 1 |
| RGG | Arginine glycine rich domain |
| ROS | Reactive oxygen species |
| RRM | RNA recognition motif |
| RNA | Ribonucleic acid |
| RNAi | RNA interference |
| RTE | Retrotransposable element |
| RT-PCR | Reverse transcriptase polymerase chain reaction |
| sALS | Sporadic amyotrophic lateral sclerosis |
| SF2 | Splicing factor 2 |
| Sf3b-1 | Splicing factor 3b subunit 1 |
| SG | Stress granule |
| siRNA | Small interfering RNA |
| SOD | Superoxide dismutase |
| SOP | Sensory organ precursor |
| TAF15 | TATA box-binding protein-associated factor 68 kDa |
| TARDBP | TAR DNA-binding protein |
| TARGET | Temporal and regional gene expression targeting |
| TBPH | TAR DNA-binding protein-43 homolog |
| TCERG1 | Transcription elongation regulator 1 |
| TDP-43 | TAR DNA-binding protein 43 |
| TDPBR | TDP-43 binding region |
| Ter94 | Transitional endoplasmic reticulum 94 |
| TLS | Translocated in liposarcoma |
| TMPyP4 | 5,10,15,20-Tetrakis-(N-methyl-4-pyridyl)porphine |
| UAS | Upstream activating sequence |
| UBPY | Ubiquitin isopeptidase Y |
| UPR | Unfolded protein response |
| UTR | Untranslated transcribed region |
| VCP | Valosin-containing protein |
| Wnd | Wallenda |
| WT | Wildtype |
| XPO1 | Exportin 1 |
| Zfp106 | Zing finger protein 106 |
| Zn | Zinc |
| ZnF | Zinc finger domain |