Table 3. Clinical phenotypes of CHF/CS/CD.

Phenotype	Clinical features
Portal hypertension*	Variceal bleeding, hepatosplenomegaly, thrombocytopenia
Cholestasis#	Recurrent cholangitis, sepsis, pruritus, intrahepatic lithiasis
Mixed	Both portal hypertension and cholestasis phenotypes
Latent	Late-onset presentation

*, most common form; ^#, usually associated to CS.