Antibodies |
Anti-His6-Tb |
Cisbio |
CAT# 61HISTLF |
Anti-MBNL1 |
EMD Millipore Corporation |
CAT# MABE70 |
Anti-mouse IgG AlexaFluor488 |
Thermo Scientific Pierce |
CAT# 7074 |
Chemicals, Peptides, and Recombinant Proteins |
Streptavidin XL-665 |
Cisbio |
CAT# 610SAXLF |
MBNL1-His6 protein |
Expressed as described in (Chen et al., 2012) |
N/A |
Critical Commercial Assays |
qScript cDNA synthesis |
Quanta BioSciences |
CAT# 101414-100 |
Quick-RNA Miniprep Kit |
Zymo |
CAT# R1055 |
TRIzol Reagent |
Thermo Fisher Scientific |
CAT# 15596026 |
WST-1 Reagent |
Roche |
CAT# 5015944001 |
CellTiter-Glo 2.0 |
Promega |
CAT# G9242 |
SSIII reverse transcriptase |
Life Technologies |
CAT# 18080085 |
GoTaq DNA polymerase |
Promega |
CAT# M8295 |
SYBR Green Master Mix |
Life Technologies |
CAT# 4368708 |
Experimental Models: Cell Lines |
DM1 Fibroblasts |
Coriell Institute |
GM03987 |
Healthy Fibroblasts |
Coriell Institute |
GM07492 |
DM1 conditional MyoD fibroblasts |
Arandel et al., 2017 |
N/A |
Healthy conditional MyoD fibroblasts |
Arandel et al., 2017 |
N/A |
F35T (FECD patient-derived corneal endothelial cells) |
Albert S. Jun, M.D., Ph.D.; Wilmer Eye Institute, Johns Hopkins Medical Institutions |
N/A |
F20T (wild-type corneal endothelial cells) |
Albert S. Jun, M.D., Ph.D.; Wilmer Eye Institute, Johns Hopkins Medical Institutions |
N/A |
Experimental Models: Organisms/Strains |
Mouse: HSA LR20b |
Mankodi et al., 2000 |
N/A |
Mouse: FVB/NJ |
The Jackson Laboratory |
001800 |
Oligonucleotides |
5’-Biotin-GCG(CUG)12-CGC |
Dharmacon |
N/A |
Control siRNA (ON-TARGET plus) |
Dharmacon |
CAT# D-001810-04-05 |
siRNA-XRN1 (ON-TARGET plus) |
Dharmacon |
CAT# J-013754-11-0002 |
siRNA-DIS3 (ON-TARGET plus) |
Dharmacon |
CAT# J-015405-110002 |
siRNA-hRRP6 |
Dharmacon (Kammler et al., 2008) |
N/A |
Primers used for RT-qPCR, see Table S1
|
Integrated DNA Technologies |
N/A |
5’DY547-2’OMe-(CAG)6
|
Integrated DNA Technologies |
N/A |
5’-Cy5-GCG(CUG)12-CGC |
Dharmacon |
N/A |
5’-Cy5-GCG(CAG)12-CGC |
Dharmacon |
N/A |
5’-Cy5-GCG(CUG)6(CAG)6-CGC |
Dharmacon |
N/A |
5’-Cy5-r(G4C2)8
|
Dharmacon |
N/A |
5’-Cy5-CGCGAATTCGCGTTTTCGCGAATTCGCG |
Integrated DNA Technologies |
N/A |
Software and Algorithms |
ImageJ |
NIH |
https://imagej.nih.gov/ij/download.html |
Olympus Fluoview Software Version 3.0 |
Olympus |
http://www.olympuscanada.com/cpg_section/cpg_support_downloads.asp?id=1274 |
GraphPad Prism 7 |
GraphPad Prism Software, Inc. |
https://www.graphpad.com/scientific-software/prism/ |
Nucgen module of AMBER 16 |
AMBER 2016 |
https://ambermd.org/GetAmber.php |