Table 2.
Management of patients with right atrial isomerism (n = 48)
| Serial no. | Procedure performed | No. of patients | Remarks |
|---|---|---|---|
| 1 | Biventricular repair (partial AV canal repair) | 1 | Alive, on follow-up moderate MR |
| 2 | Systemic artery to pulmonary artery shunt | 3 | Survived to next stage |
| 3 | Bidirectional cavo-pulmonary shunt | 30 | Survived to next stage |
| With TAPVC repair | 4/30 | ||
| 4 | Extra-cardiac Fontan completion | 20 | 2/20 expired |
| With AV valve repair | 2/20 | ||
| With AV valve replacement | 1/20 | ||
| With pacemaker implantation | 1/20 | ||
| 5 | AV valve re-replacement in a patient with Fontan + AV valve replacement | 1 | Expired |
| 6 | TAPVC repair | ||
| With PA banding | 1 | Expired | |
| BT shunt | 1 | Expired | |
| 7 | Catheter-based interventions | 2 | |
| Balloon pulmonary valvotomy | 1/2 | Unsuitable for single ventricle repair strategy | |
| RVOT stenting | 1/2 | ||
| 8 | No interventions performed | 12 | |
| High PA pressure | 6 | ||
| Parents refused surgery | 5 | ||
| Absent central PA’s | 1 | ||