Table 3.
Management of patients with left atrial isomerism (n = 27)
| Serial no. | Procedure performed | No. of patients | Remarks |
|---|---|---|---|
| 1 | Biventricular repair | 4 | All alive and under follow-up |
| Atrial septation | 1 | ||
| Atrial septation + AV valve repair | 2 | ||
| Repair of eventration of diaphragm + ASD closure | 1 | ||
| 2 | Systemic artery to pulmonary artery shunt | 1 | Progressed to next stage |
| 3 | Pulmonary artery banding | 3 | 1 progressed to next stage; 2 unsuitable for cavo-pulmonary shunt due to high PA pressure |
| 4 | Total cavo-pulmonary shunt (Kawashima) | 14 | 1 late death |
| 5 | Extra-cardiac Fontan completion | 4 |
All 4 had extensive PAVMs 1 postoperative death (cardiac tamponade) |
| 6 | No interventions performed | ||
| Awaiting Kawashima procedure | 4 | ||
| High pulmonary artery pressure | 2 | ||
| No intra-cardiac defect (only atrial tachycardia) | 1 | ||