α-ACT	α-Actinin
CRISPR	Clustered regularly interspaced short palindromic repeats
cTnT	Cardiac troponin T
ER	Endoplasmic reticulum
FBL	rRNA methyltransferase fibrillarin
GRP75	75-kDa Glucose regulated protein
GRP78	78-kDa Glucose-regulated protein
HERP	Homocysteine-inducible ER stress protein
iPSCs	Induced pluripotent stem cells
iPSC-CMs	iPSC-derived cardiomyocytes
MAMs	Mitochondria-associated membranes
MFN2	Mitofusin-2
NCL	Nucleolin
OA	Organic acidemia/aciduria
OCR	Oxygen consumption rate
PA	Propionic acidemia
PBS	Phosphate buffered saline
PCC	Propionyl-CoA carboxylase
POLR1A	Large subunit of Pol I
PPAR	Peroxisome proliferator activated receptors
qRT-PCR	Real-time quantitative reverse transcription- polymerase chain reaction
RRN3	pol I-pecific transcription initiation factor
SIG-1R	Sigma-1 receptor
SIRT7	Pol I-activating NAD-dependent histone deacetylase sirtuin 7
SMA	Alpha-smooth muscle actin
UBTF	Ribosomal RNA upstream binding transcription factor
UPR	Unfolded protein response
WT	Wild-type