Figure. Echocardiographic Appearance and Distribution of the Different Subtypes of BAV in the Group of Newborns With BAV, Classified According to Sievers and Schmidtke⁵.

Prevalence and 95% CIs for the bicuspid aortic valve (BAV) subtypes: type 0, anterior-posterior in 10 (5.1% [95% CI, 5.1%-27.9%]) and lateral in 7 (3.6% [95% CI, 3.6%-17.4%]); type 1 in 178 (90.8% [95% CI, 86.0%-94.1%]) (147 [75.0% {95% CI, 68.5%-80.5%}] right-left coronary raphe; 27 [13.8% {95% CI, 9.6%-19.3%}] right noncoronary raphe; 4 [2.0% {95% CI, 0.8%-5.1%}] nonleft coronary raphe); and type 2 in 1 (0.5% [95% CI, 0.1%-2.8%]).

^aThe other types are not shown; see eFigure 1 in the Supplement for complete schematic.