Table 1.
Demographics | n = 54 | Remarks |
---|---|---|
Male | n = 43 | |
Female | n = 11 | |
Age in years at onset KD (median, range) | 3.1 (0.12–11.15) | Age-at-onset was unknown in two patients. |
Missed diagnosis, no treatment | n = 7 | No treatment (IVIG/prednisone) received in seven cases, of which two did receive ASA. |
Day of treatment after onset of fever (median, range) | 8 (4–26) | In 2 patients the day of treatment was unclear. |
Treatment > 10 days after fever onset | n = 11 | |
Non-responder to 1st IVIG | n = 11 | Persistent fever > 48 h after IVIG treatment. |
ΔTime in years (time between CMR and cCTA) (median, range) | 3 (0–7) | In 3 patients the cCTA was performed after the CMR. ΔTime in years (time between cCTA and CMR) for these patients was 1, 1, and 4 years. |
CAA Z- score acute stage | ||
• Z-score > 10* (giant) | n = 12 | |
• Z-score 3–10* (small- to medium-sized aneurysms) | n = 13 | |
• Z-score <3* (no aneurysm) | n = 23 | |
• Unknown | n = 6 |
CAA status is based on prior echocardiography results in the acute phase of KD.