Table 1A.

Pediatric vasculitis cohort.

ID	Diagnosisa	Onsetb	Sex	ANCA	Renalc	Treatmentd
1	uAAV	16	Male	MPO	No	prednisone
2	MPA	15	Female	MPO	Yes	prednisone
3	GPA	12	Female	MPO	Yes	none
4	GPA	11	Female	MPO	Yes	prednisone
5	GPA	12	Female	MPO	No	prednisone, methotrexate
6	UCV	17	Female	MPO	Yes	prednisone, cyclophosphamide
7	GPA	15	Male	MPO	Yes	none
8	GPA	5	Female	MPO	Yes	prednisone, methotrexate, rituximab, azathioprine
9	GPA	16	Female	MPO	Yes	none
10	GPA	2	Male	MPO	Yes	none
11	GPA	13	Female	MPO	Yes	none
12	GPA	17	Female	MPO	Yes	prednisone, cyclophosphamide, rituximab
13	GPA	15	Male	MPO	Yes	prednisone
14	UCV	17	Female	MPO	Yes	none
15	MPA	16	Male	MPO	Yes	none
16	MPA	17	Female	MPO	Yes	cyclophosphamide
17	GPA	17	Male	MPO	Yes	prednisone, cyclophosphamide
18	GPA	1	Female	MPO	Yes	prednisone, rituximab
19	GPA	5	Female	MPO	Yes	prednisone, cyclophosphamide
20	MPA	5	Female	MPO	Yes	prednisone
21	GPA	10	Male	PR3	Yes	none
22	GPA	15	Female	PR3	Yes	none
23	GPA	13	Female	PR3	Yes	prednisone
24	GPA	15	Male	PR3	Yes	none
25	NA	17	Female	PR3	Yes	prednisone
26	GPA	12	Female	PR3	Yes	prednisone, rituximab
27	GPA	15	Male	PR3	Yes	prednisone
28	GPA	15	Female	PR3	Yes	prednisone, rituximab
29	uAAV	12	Female	PR3	No	prednisone, methotrexate
30	GPA	14	Male	PR3	No	prednisone, rituximab
31	GPA	14	Female	PR3	Yes	none
32	GPA	14	Female	PR3	Yes	prednisone, cyclophosphamide
33	uAAV	13	Male	PR3	Yes	prednisone
34	UCV	13	Female	PR3	Yes	prednisone, cyclophosphamide
35	GPA	12	Female	PR3	Yes	prednisone, cyclophosphamide
36	GPA	12	Female	PR3	Yes	prednisone, cyclophosphamide, rituximab
37	UCV	14	Female	PR3	Yes	prednisone
38	GPA	15	Female	PR3	Yes	prednisone, cyclophosphamide, rituximab
39	GPA	14	Female	PR3	Yes	prednisone, rituximab
40	GPA	15	Male	PR3	Yes	prednisone, rituximab
41	GPA	18	Male	PR3	Yes	prednisone, rituximab
42	GPA	16	Male	PR3	Yes	prednisone, rituximab
43	GPA	16	Male	PR3	yes	prednisone, rituximab
44	MPA	13	Male	Both	Yes	none
45	uAAV	10	Female	Negative	No	prednisone
46	uAAV	9	Male	Negative	No	prednisone
47	cPAN	2	Male	Negative	Yes	prednisone, infliximab
48	UCV	15	Female	Negative	Yes	prednisone
49	GPA	7	Female	Negative	Yes	none
50	UCV	4	Male	Negative	No	prednisone
51	PAN	16	Female	Negative	No	none

^aAccording to the EMA classification algorithm (21). MPA, microscopic polyangiitis; GPA, granulomatosis with polyangiitis; PAN, polyarteritis nodosa; uAAV, unclassified ANCA-associated vasculitis, UCV, unclassified vasculitis. ^bAge in years when symptoms associated with vasculitis first presented ^cRenal involvement determined by renal component of the pVAS => 4 ^dCurrent treatments at diagnosis, coincident with sample and data collection.