Table 1.

Summary of primary peritoneal and diaphragmatic clear cell carcinomas reported in the literature.

Case	Authors	Age	Past history or concurrence of endometriosis or adenomyosis	Serum CA125 (U/mL)	Tumor size	Location	Peritoneal dissemination	CT findings	MR findings	Macroscopic findings	Coexistent endometriosis with CCC on the histopatlogy	Treatment	Outcome
1	Evans et al.	54	Ov EM, AM	NA	18 × 13 cm	Sigmoid mesocolon	No	Multilocular cyst with nodules	NA	Multilocular cyst with nodules	No	DS followed by RT	NA
2	Lee et al.	67	None	2218	6 cm	Abdomen, Pelvs	Yes	NA	NA	NA	No	DS with TAH + BSO	NA
3	Tziortzioti et al.	62	None	313.9	0.5–2 cm	Subdiaphragm, Abdomen, Omentum	Yes	NA	NA	NA	No	DS with TAH + BSO, CTx	DOD at 6 months
4	Ichimura et al.	45	Ov EM	28	NA	Pelvis	No	Cyst with solid components	NA	NA	No	DS with TAH + BSO, CTx	RD at 32 months
5	Hama et al.	53	EM	467	NA	Pelvis, Liver surface	Yes	Cystic mass with solid coponents	Multicystic mass with hemorrhage and heterogenous solid protrusions	NA	No	DS and BSO	DOD at 5 months
6	Terada et al.	49	None	NA	3 cm, 2 cm	Greatur curvature of the stomach, Splenic hilus	No	NA	NA	Cystic tumor with solid and papillary components	No	DS	DOD at 6 months
7	Takano et al.	53	None	467	13 × 5 cm	Between liver and disphargm, Omentum, Abdomen	Yes	NA	NA	NA	No	DS	DOD at 5 months
8	Takano et al.	66	None	347	20 × 15 cm	Omentum	No	NA	Cystic and solid mass	NA	No	DS with TAH + BSO, omentectomy, lymph node dissection, CTx	NED at 20 months
9	Muezzinoglu et al.	54	pEM	42.3	25 × 25 × 4 cm	Abdomen	No	NA	Cystic mass with solid nodules	Mulicystic tumor with papillary structures and solid nodules	Yes	DS with TAH + BSO, CTx	NED at 12 months
10	Johnson et al.	54	None	NA	5.6 × 3.7 × 3.5 cm	Pelvis	No	Soft tissue mass	NA	NA	No	CTx and RTx	RD (bone and liver)
11	Shigeta et al.	59	AM, pEM	76	7 cm	Pelvis	No	NA	Heterogenous tumor	Multilocular cystic tumor with solid components	No	DS with TAH + BSO, PLD, CTx	NED at 5 months
12	Insabato et al.	49	None	NA	9.5 × 9 × 7 cm	Adherent to the ileum	No	Solid and cystic mass	NA	Microcystc and solid tumor	No	DS with left oophorectomy	RD at 6 months(Inguinal lymphnode), NED at 5 months after second surgery and CTx
13	Peiro et al.	48	None	57	25 × 15 cm	Abdomen	No	Cystic mass wth papillary projection	NA	Multilocular cystic tumor with papillary components	No	DS with T1H + BSO + omentectomy	RD at 8 months (peritoneum), stable at 28 months after initial surgery by CTx
14	Fujiu et al.	65	Ov EM	48	2.5 cm	Right diaphragm	No	Thick-walled cystic mass with peripheral enhancement	Thick-walled cystic mass with peripheral enhancement	Thick-walled unilocular cyst with protruded components	No	DS	RD at 12 months (lung)
15	Harimoto et al.	55	None	NA	3 cm	Right diaphragm	No	Lobulated cystic mass	Lobulated cystic mass	Lobulated cystic tumor with protruded components and intracystic hemorrhage	No	DS	NA
16	Present case	55	Ov EM, pEM	40	5.5 × 4.8 cm	Right diaphragm	No	Cyst with solid and papillary components	Cyst with solid and papillary components	Cyst with solid and papillary components	Yes	DS and Cx	NED at 15 months

Ov EM, ovarian endometriosis; pEM, peritoneal endometriosis; AM, adenomyosis; CCC, clear cell carcinoma; NA, not available DS, debulking surgery; TAH, total abdominal hysterectomy; BSO, bilateral salpingo-oophorectomy; CTx, chemotherapy; RTx, radiotherapy; DOD, death of disease; NED, no evidence of isease; RD, recurrence of disease.