ER |
Endoplasmic Reticulum |
ERdjs |
ER-resident DnaJ-like Proteins |
NEF |
Nucleotide Exchange Factors |
MSS |
Marinesco-Sjögren Syndrome |
ERQC |
ER Protein Quality Control |
HSP |
Heat Shock Protein |
UPS |
Ubiquitin Proteasomal System |
ERAD |
ER-associated Degradation |
CNX |
Calnexin |
CRT |
Calreticulin |
Ig |
Immunoglobulin |
UPR |
Unfolded Protein Response |
ATP |
Adenosine Triphosphate |
NBD |
Nucleotide-binding Domain |
SBD |
Substrate-binding Domain |
SRP |
Signal Recognition Particle |
Sil1 |
Suppressor of Ire1 and Lhs1 deletion 1 |
BAP |
BiP-associated Protein |
ARM |
Armadillo-like Repeats |
PBMCs |
Peripheral Blood Mononuclear Cells |
AARS |
Alanyl tRNA Synthetase |
IR |
Insulin Receptor |
IGF1R |
Insulin-like Growth Factor Receptor |
MIGIRKO |
Muscle-Specific Dual Knockout of IR And IGF1R |
NMJ |
Neuromuscular Junctions |
LBLs |
Lymphoblastoid Lines |
i.p.GTT |
Intraperitoneal Glucose Tolerance Test |
i.p.ITT |
Intraperitoneal Insulin Tolerance Test |
ALS |
Amyotrophic Lateral Sclerosis |
PHGDH |
Phosphoglycerate dehydrogenase |
ATXN10 |
Ataxin-10 |
PBA |
4-Phenylbutyrate |
TUDCA |
Tauroursodeoxycholic Acid |
SCA10 |
Spinocerebellar Ataxia Type 10 |
RIPK1 |
Receptor-interacting Serine/Threonine-Protein Kinase 1 |