AM	Alveolar macrophages
BATF3	Basic leucine zipper transcriptional factor ATF-like 3
BMPR2	Bone morphogenetic protein receptor type 2
cDC1s	Type 1 conventional DCs
cDC2s	Type 2 conventional DCs
CTD-PAH	Connective tissue disease PAH
CXCL8	X-X-C-motif chemokine ligand 8
DCs	Dendritic cells
EvG	Elastic von Gieson
H&E	Hematoxylin and eosin
HPAH	Heritable PAH
i.p.	Intraperitoneal
i.t.	Intratracheally
IL	Interleukin
IM	Interstitial macrophages
IPAH	Idiopathic PAH
LPS	Lipopolysaccharide
LV	Left ventricle
Mo-DC	Monocyte-derived-DC
NaCl	Sodium chloride
NF-kB	Nuclear factor-kappa B
PAH	Pulmonary arterial hypertension
PAP	Pulmonary arterial pressure
PASMCs	Pulmonary artery smooth muscle cells
PH	Pulmonary hypertension
pDC	Plasmacytoid DC
PFA	paraformaldehyde
Poly I:C	Polyinosinic-polycytidylic acif high molecular weight
RV	Right ventricle
RVSP	Right ventricular systolic pressure
S	Septum
TGFβ	Transforming growth factor-β
TLOs	Tertiary lymphoid organs
TLR	Toll like receptor
Tnfaip3	TNFα-induced protein-3
WHO	World health organization
WT	Wild type
α-SMA	Alpha smooth muscle actin