| AAT | Alpha 1-antitrypsin |
| AATD | Alpha 1-antitrypsin deficiency |
| ATG | Autophagy-related protein |
| CBZ | Carbamazepine |
| CMA | Chaperone-associated autophagy |
| eMI | Endosomal micro-autophagy |
| ER | Endoplasmic Reticulum |
| ERAD | Endoplasmic reticulum-associated degradation |
| ERLAD | ER-to-lysosome-associated degradation pathway |
| ESCRT | Endosomal sorting complex required for transport |
| GABARAP | γ-aminobutyric acid receptor-associated protein |
| GIM | GABARAP interaction motif |
| hsc70 | Protein heat shock cognate protein 70-kDa |
| IB | Inclusion bodies |
| iPSC | Induced pluripotent stem cells |
| LAMP-2A | Lysosome-associated membrane protein type 2A |
| LC3 | Light chain 3 |
| LIM/LIR | LC3 interaction motif/region |
| MVB | Multivesicular bodies |
| NFκB | Nuclear factor-κB |
| norUDCA | nor-urso-deoxycholic acid |
| PI | Protease Inhibitor |
| PAS | Periodic acid-Schiff |
| ULK1 | Unc-51 like autophagy activating kinase 1 |
| UPS | Ubiquitin–proteasome system |
| TFEB | Transcription factor EB |
| WIPI | WD repeat domain phosphoinositide-interacting |
| ZZ | Homozygous Z patient |