Table 2.
PAS-positive inclusion deposits in the myocardium of ten patients with GSD IV pre-or-post liver transplantation.
| References | Case | Time sample (months posttransplant) | Mean % area occupied by inclusions | No of inclusions per 3.6 × 105 μm2 | Mean size of inclusions (μm2) |
|---|---|---|---|---|---|
| Aksu et al. (3) | 1 | Pretransplant | – | – | – |
| Willot et al. (25) | 3 | 76.0 (Autopsy) | – | – | – |
| 4 | 11 (Autopsy) | 50% | – | – | |
| Sokal et al. (26) | 5 | 9.0 | – | – | – |
| Selby et al. (23, 28) | 7 | 54.0 | 0.5% | 24 | 140 |
| 9 | 1.2 (Autopsy) | 2% | 46 | 141 | |
| 12 | 0.9 | 13 % | 332 | 146 | |
| 14.0 | 5.9% | 129 | 164 | ||
| 13 | 1.0 | Too few to quantitate | |||
| 11.0 | Too few to quantitate | ||||
| Alshak et al. (30)Rosenthal et al. (31) | 15 | 30.0 (Autopsy) | – | – | – |
| Magoulas et al. (2) | 17 | 4.0 (Autopsy) | – | – | – |