Table 1.
Comparison of clinical, and laboratory characteristics between XL-CGD, and AR-CGD.
| Parameter | XL (n = 77) | AR (n = 97) | p value |
|---|---|---|---|
| Median age at onset of infections (IQR)a | 6 months (3–20) | 12 months (3–35) | 0.074 |
| Median age at diagnosisa | 12 months (7–24) | 30 (9–86) | 0.002 |
| Median delay in diagnosis of CGDa | 6 months (1.5–19) | 9.2 (1.5–33) | 0.353 |
| Median follow-upa | 1.16 year (1–2.76) | 1 year (0.10–2.8) | 0.735 |
| Median stimulation index in DHRa | 1.2 (1–2.76) | 1.34 (0.98–2.2) | 0.741 |
| Number of patients with >3 infectious episodesb | 19 | 15 | 0.100 |
| Episodes of pneumoniab | 45 | 70 | 0.003 |
| Number of patients with >3 episodes of pneumoniab | 9 | 3 | 0.007 |
| Episodes of superficial abscessesb | 20 | 22 | 0.462 |
| Episodes of deep abscessesb | 6 | 7 | 0.488 |
| Episodes of lymphadenitisb | 20 | 27 | 0.272 |
| Episodes of osteomyelitisb | 9 | 9 | 0.510 |
| Episodes of liver abscessesb | 6 | 10 | 0.500 |
| Episodes of septicemiab | 8 | 6 | 0.540 |
| Number of patients with mycobacterial diseaseb | 10 | 20 | 0.105 |
| Number of patients with mortalityb | 18 | 23 | 1.000 |
| Median Stimulation index <1.5 in DHRb | 31 | 44 | 0.672 |
aMann–Whitney U test.
bFisher’s exact test or chi-squared test.