Table 3.
Therapeutic management of TMA patients.
| Treatment, n (%) | Primary TMA | Secondary TMA | ||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| All | TTP | aHUS | tHUS | HELLP syndrome | Malignant HBP | Malignancies | Drugs | Infections | AID | aGVHD | Others | |
| n = 216 | n = 12 | n = 8 | n = 8 | n = 79 | n = 12 | n = 30 | n = 11 | n = 5 | n = 5 | n = 16 | n = 30 | |
| Plasma exchange | 40 (18.5) | 9 (75.0) | 6 (75.0) | 6 (75.0) | 0 (0) | 1 (8.3) | 5 (16.6) | 3 (27.3) | 2 (40.0) | 3 (60.0) | 1 (6.25) | 4 (13.3) |
| Plasma infusion | 30 (13.9) | 2 (16.6) | 2 (25.0) | 2 (25.0) | 10 (12.7) | 0 (0) | 3 (10.0) | 3 (27.3) | 0 (0) | 0 (0) | 2 (12.5) | 6 (20.0) |
| PE or PI | 61 (28.2) | 9 (75.0) | 6 (75.0) | 6 (75.0) | 10 (12.7) | 1 (8.3) | 6 (20.0) | 6 (54.5) | 2 (40.0) | 3 (60.0) | 3 (18.8) | 9 (30.0) |
| Eculizumab | 8 (3.7) | 1 (8.3) | 3 (37.5) | 2 (20.0) | 0 (0) | 0 (0) | 1 (3.3) | 1 (9.1) | 0 (0) | 0 (0) | 0 (0) | 0 (0) |
| Rituximab | 17 (7.9) | 6 (50.0) | 1 (12.5) | 0 (0) | 0 (0) | 0 (0) | 3 (10.0) | 0 (0) | 0 (0) | 2 (40.0) | 4 (25.0) | 1 (3.3) |
| Red blood cell transfusion | 94 (43.5) | 8 (66.7) | 4 (50.0) | 4 (50.0) | 14 (17.7) | 6 (50.0) | 19 (63.3) | 5 (45.4) | 2 (40.0) | 4 (80.0) | 15 (93.8) | 13 (43.3) |
| Platelet transfusion | 49 (22.7) | 3 (25.0) | 1 (12.5) | 1 (12.5) | 7 (8.9) | 1 (8.3) | 12 (40.0) | 5 (45.4) | 0 (0) | 0 (0) | 14 (87.5) | 5 (16.6) |
| Dialysis (during first admission) | 51 (23.6) | 3 (25.0) | 6 (75.0) | 3 (37.5) | 6 (7.59) | 10 (83.3) | 5 (16.7) | 3 (27.3) | 3 (60.0) | 2 (40.0) | 2 (12.5) | 8 (26.7) |