Table 1.

ADAMTS13 activity and inhibitor at presentation and during follow-up.

	09.01.2018	15.03.2018	15.10.2018	01.11.2018
ADAMTS13 activity, % (40–130)	<3.0*	<3.0*	<1.0**	<1.0**
ADAMTS13 concentration, μg/ml (0.31−0.82)	<0.01*
ADAMTS13 inhibitor, Bethesda Units (<0.5)			0**	0**
ADAMTS13 IgG antibodies, U/ml (<12)	1.1*

^*Values measured at Institute of Transfusion Medicine and Clinical Hemostasiology, St. Georg Hospital Leipzig, Germany (Technozym^® ADAMTS13 ELISA Kit and TECHNOZYM ADAMTS13 INH, measuring anti-ADAMTS13 antibodies by ELISA)

^**ADAMTS13 activity and functional inhibitor measured by in house assay using the FRETS-VWF73 substrate (1, 2) at the Institute of Clinical Chemistry and Laboratory Medicine, University Medical Center Mainz, Germany.