Table 3.
Descriptive analysis of demographic and clinical characteristics by region for each of the diagnostic categories. Primary Lateral Sclerosis (PLS).
| Demographic and clinical characteristics stratified by region | ||
|---|---|---|
| Valencia (n = 10) | Catalonia (n = 4) | |
| Variables | ||
| Sex [n (%)] | ||
| Women | 5 (50.0) | 3 (75.0) |
| Men | 5 (50.0) | 1 (25.0) |
| Age at diagnosisa | 59.20 (12.48) | 56.00 (12.52) |
| 60 (55.75–68.25) | 60.5 (42.75–64.75) | |
| (28–73) | (38–65) | |
| Age at diagnosis in quintiles [n (%)] | ||
| < = 53/ < = 52 | 1 (10.0) | 1 (25.0) |
| (53–59]/(52–61] | 3 (30.0) | 1 (25.0) |
| (59–66]/(61,67] | 3 (30.0) | 2 (50.0) |
| (66–71]/(67,74.6] | 2 (20.0) | 0 (0.0) |
| > 71/ > 74.6 | 1 (10.0) | 0 (0.0) |
| Symptom at onset [n (%)] | ||
| Bulbar | 3 (30.0) | NA |
| Spinal | 7 (70.0) | NA |
| Respiratory | 0 (0.0) | NA |
| Cognitive (dementia) | 0 (0.0) | NA |
| C9orf72 [n (%)] | 0 (0.0) | 0 (0.0) (n = 3) |
| SOD1 [n (%)] | 0 (0.0) |
0 (0.0) (n = 0) No test available |
aFirst row: mean (sd).
Second row: median (1st–3rd quartiles).
Third row: (min–max).