fig 6.

Case 1: 16-year-old boy with VHLD.

A, Contrast-enhanced sagittal T1-weighted TSE image (700/12/2) shows a large, well-demarcated, intensely and heterogeneously enhancing intramedullary tumor at C7–T2. Note vascular flow voids in and around the tumor (curved arrows) and superficial enhancement of the spinal cord (straight arrows), proved to be dilated perimedullary veins at surgery. Syrinx extends from medulla oblongata to T12. Also note multiple small intensely and homogeneously enhancing tumors, most of which are located superficially at the posterior aspect of the spinal cord.

B, Contrast-enhanced axial T1-weighted SE image (660/15/1) at C7–T1 shows enlargement of the spinal canal and the enhancing tumor. The tumor occupies entire dural sac and the spinal cord is barely discernible. The tumor was interpreted as deeply located within the spinal cord on MR image, and was confirmed at surgery.