| ALS | amyotrophic lateral sclerosis |
| ALS-FRS | amyotrophic lateral sclerosis functional rating scale |
| ChAT | choline acetyltransferase |
| CFuPN | corticofugal projection neurons |
| Crym | mu-crystallin |
| CTIP2 | COUP TF1-interacting protein 2 (now designed as Bcl11b: BAF chromatin remodeling complex subunit BCL11B) |
| C9-BAC | C9ORF 72 BAC transgenic mice |
| DTI | diffusion tensor imaging |
| EMG | electromyography |
| ES | end stage |
| Fezf2 | FEZ Family Zinc Finger 2 |
| FG | fluorogold |
| hPFN1 | human Profilin 1 |
| ISH | in situ hybridization |
| LMN | lower motor neurons |
| MRI | magnetic resonance imaging |
| NMJ | neuromuscular junctions |
| SOD1 | superoxyde dismutase 1 |
| SubCerPN | subcerebtral projection neurons |
| TDP-43 | TAR DNA binding protein 43 |
| UMN | upper motor neurons |
| WT | wild type |