Figure 1.

Diagram showing different treatment regimens in patients with IgG4-RD. IgG4-RD: IgG4-related disease; RTX: rituximab; * a patient lost to follow-up after steroid pulse therapy; ^a a patient with histologically confirmed IgG4-RD not on medication, who died from complications after surgery for suspected cancer; ^b a patient treated after relapse with steroids, who died from intraductal papillary mucinous neoplasm that progressed to pancreatic cancer; ^c a patient who had been treated with steroid pulse therapy and RTX (as a last resort) but died from sepsis.